MRCP UK EXAMINATIONS

CARDIOLOGY

PROSTHETIC HEART VALVES

Question [CLICK ON ANY CHOICE TO KNOW THE RIGHT ANSWER]
Rhabdomyoma is typically associated with ____
A
arrhythmias
B
LVOTO
C
tuberous sclerosis
D
all of the above
Explanation: 

Detailed explanation-1: -Most cardiac rhabdomyomas are associated with tuberous sclerosis (TS) and appear in the ventricular myocardium, the atria, the cavoatrial junction, or the epicardial surface.

Detailed explanation-2: -Cardiac rhabdomyoma may be associated with arrhythmias (irregular heartbeats), which can potentially be life threatening. The kinds of arrhythmias associated with cardiac rhabdomyomas include supraventricular tachycardia and ventricular tachycardia.

Detailed explanation-3: -Rhabdomyoma is a benign tumor that shows skeletal muscle differentiation. Rhabdomyomas are classically divided into those that occur in the heart and those occur outside the heart. Cardiac rhabdomyomas are frequently associated with tuberous sclerosis.

Detailed explanation-4: -Cardiac rhabdomyoma is a benign tumor which constitutes the most common cardiovascular feature of the tuberous sclerosis complex, a multisystem genetically determined neurocutaneous disorder.

There is 1 question to complete.