MRCP UK EXAMINATIONS

Detailed explanation-1: -In Ebstein anomaly, the tricuspid valve sits lower than normal in the right ventricle. This makes it so that a portion of the right ventricle becomes part of the right atrium, causing the right atrium to enlarge and not work properly.

Detailed explanation-2: -Ebstein’s anomaly is a defect of the tricuspid valve. The tricuspid valve separates the right atrium (the chamber that receives blood from the body) from the right ventricle (the chamber that pumps blood to the lungs). In Ebstein’s anomaly, two leaflets of the tricuspid valve are not in the right place.

Detailed explanation-3: -Symptomatic neonates with Ebstein’s anomaly have a poor prognosis. Marked cardiac enlargement, advanced echocardiographic severity score, cyanosis, and severe regurgitation of the tricuspid valve all predict neonatal death without surgery.

Detailed explanation-4: -The right ventricle becomes split into two portions. The first portion is the “atrialized” right ventricle, where the right ventricular inflow should typically be, extending from the undisplaced tricuspid annulus to the “functional” right ventricle. The second portion is the functional right ventricle.